ABSTRACT
Sprengel deformity is a rare congenital disorder characterized by a congenital high scapula caused by obstruction of the development of the scapula, which accompanies bone, muscle and cartilage during pregnancy. This scapular deformity can be associated with other congenital malformations such as rib abnormalities, scoliosis, and Klippel-Feil syndrome. This is a follow-up of 3-year-old children with Sprengel deformity, cavendish grade 3 who were treated with the Woodward procedure. Authors conclude that the Woodward procedure is an effective procedure for obtaining good functional and cosmetic results.
ABSTRACT
Arthrogryposis includes heterogeneous disorders, characterized by congenital contractures of multiple joints. Knee involvement is very common (38–90 % of patients with amyoplasia) ranging from soft-tissue contractures (in flexion or hyperextension) to subluxation and dislocation. Children who present late will require surgery involving quadricepsplasty or lengthening of the contracted quadriceps muscle. Curtis and Fisher describe an open V-Y lengthening of the quadriceps femoris with post-operative immobilization in 30-45 ° of flexion. The main issue of this technique was limited degree of flexion that can be achieved, and the fibrous replacement of the quadriceps muscle. This is a neglected case of hyperextension deformity and congenital dislocation of knee in children with arthrogryposis resistant to conservative management and successfully treated by open quadricepsplasty.